authors
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Krzysztof Bar 1, Robert Klijer 1, Elżbieta Czekajska-Chehab 3, Waldemar Białek 1, Jerzy Michalak 1, Lech Wronecki 2
- 1 Katedra i Klinika Urologii Akademii Medycznej w Lublinie
Kierownik: prof. AM dr hab. Krzysztof Bar
2 Katedra i Zakład Patomorfologii Klinicznej Akademii Medycznej w Lublinie
Kierownik: prof. dr hab. Elżbieta Korobowicz
3 Zakład Radiologii Lekarskiej AM w Lublinie
Kierownik zakładu: prof. dr hab. Andrzej Drop
keywords
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urinary bladder, malignant tumour, pheochromocytoma
summary
- Bladder pheochromocytomas (pheochromocytoma, paraganglioma) are tumours arising from chromaffin cells in sympathetic ganglia. Most of paragangliomas are located in the adrenal medulla, while extra-adrenal localization is reported in about 10% cases. Pheochromocytoma of the urinary bladder is rare, accounting less than 0.06% of all bladder tumors. Bladder pheochromocytomas are mostly benign tumours so partial cystectomy with adequate margins is the treatment of choice for most cases. We report a case of urinary bladder pheochromocytoma with malignant clinical manifestation which required cystectomy.
references
- Deklerk DP, Catalona WJ, Nime FA, Freeman C: Malignant pheochromocytoma of the bladder: The late development of renal cell carcinoma. J Urol 1975, 113, 864-868.
- Heyman J, Cheung Y, Ghali V, Leiter E: Bladder pheochromocytoma: Evaluation with magnetic resonance imaging. J Urol 1989, 141, 1424-1426.
- Zornow DH, Bentrovato DA, Olson HW et al: Vesical-related paragangliomas. J Urol 1977, 118, 247-250.
- Mahoney EM, Harrison JH: Malignant pheochromocytoma: clinical course and treatment. J Urol 1977, 118, 225-229.
- Jurincic C, Gasser A, Metz KA et al: Pheochromocytoma of the urinary bladder. Urol Int 1992, 48, 232-234.
- Ansari MS, Goel S, Durairajan LN, Seth A: Malignant paraganglioma of the urinary bladder. A case report. Int Urol Nephrol 2001, 33, 343-345.
- Baima C, Casetta G, Vella R, Tizzani A: Bladder pheochromocytoma: a 3-year follow-up after transurethral resection (TURBT). Urol Int 2000, 65, 176-178.
correspondence
Krzysztof Bar
Klinika Urologii AM
ul. Jaczewskiego 8
20-950 Lublin
tel. 081 72 44 794
kl.urol.lublin@interia.pl
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