BIG ANGIOMYOLIPOMA OF THE KIDNEY
IN TUBEROUS SCLEROSIS PATIENT
THE CASE OF ORGAN SPARING SURGERY TREATEMENT
Article published in Urologia Polska 2000/53/3.
authors
-
Krzysztof Pastewka 1, Andrzej Borówka 1, Wojciech Pypno 1, Sergiusz Jóźwiak 2
- 1 Klinika Urologii CMKP w Warszawie
Kierownik: prof. dr hab. med. A. Borówka
2 Klinika Neurologii Instytutu Pomnik Centrum Zdrowia Dziecka
Kierownik: doc. dr hab. med. S. Jóźwiak
keywords
-
kidney angiomyolipoma tuberous sclerosis
summary
- The kidney angiomyolypoma (AML) incidence in sclerosis tuberosa patients
- Bourneville syndrome
- occur hardly ever, mostly beacause of tumour's big diameter, haematuria,
- bleeding, hydronephrosis end pain. The multifocality and bilateral occurrence
- of angiomyolypoma in sclerosis tuberosa syndrome patients is very common,
- that is why the organ sparing surgery should be prefered.
- The case of partial nephrectomy because of 10 cm angiomyolipoma in 17
- year old girl with Bourneville syndrome was presented. The sclerosis tuberosa
- syndrome was discussed.
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