PTU - Polskie Towarzystwo Urologiczne
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BIG ANGIOMYOLIPOMA OF THE KIDNEY IN TUBEROUS SCLEROSIS PATIENT THE CASE OF ORGAN SPARING SURGERY TREATEMENT
Article published in Urologia Polska 2000/53/3.

authors

Krzysztof Pastewka 1, Andrzej Borówka 1, Wojciech Pypno 1, Sergiusz Jóźwiak 2
1 Klinika Urologii CMKP w Warszawie
Kierownik: prof. dr hab. med. A. Borówka
2 Klinika Neurologii Instytutu Pomnik Centrum Zdrowia Dziecka
Kierownik: doc. dr hab. med. S. Jóźwiak

keywords

kidney angiomyolipoma tuberous sclerosis

summary

The kidney angiomyolypoma (AML) incidence in sclerosis tuberosa patients
Bourneville syndrome
occur hardly ever, mostly beacause of tumour's big diameter, haematuria,
bleeding, hydronephrosis end pain. The multifocality and bilateral occurrence
of angiomyolypoma in sclerosis tuberosa syndrome patients is very common,
that is why the organ sparing surgery should be prefered.
The case of partial nephrectomy because of 10 cm angiomyolipoma in 17
year old girl with Bourneville syndrome was presented. The sclerosis tuberosa
syndrome was discussed.

references

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